|
|
|
|
Click photo to enlarge Birth Defects Cleft Lip & Cleft Palate (In Detail)Rare Cleft (In Detail) Cranio-Facial Microsomia Hypospedias Epispedias and Extrophy Syndactyly Polyactyly & Club Hand Bat Ears (In Detail) Cystic Hygromas Dermoids Rare CleftsFacial and cranial clefts other than the commonly seem cleft lip and palate are rare clefts. They are treated by multi stage surgeries to achieve a presentable appearance and a near perfect functional status before school going age.
Cranio-facial
microsomia or I and II Branchial Syndrome has a wide clinical presentation,
varying in extent, degree and combination of deformities of the jaws,
ears, soft tissues of the face and the central nervous system.. It involves,
to a variable degree, all the structures derived from the first and
second Branchial Arches and the Otic Capsule. The primary deficiency
of soft tissues and bones produce secondary effect on adjacent and otherwise
normal structures and all this together adds up to the clinical picture. With the help of a Computerised facial scan a proper clinico-radiological classification is possible and this itself decides the treatment programme. Our plan of management is taking care of the skin tags, sinuses, macrostoma and other minor soft tissue blemishes in infancy, close orthodontic supervision during the phase of mixed dentition ( 8-12 years ) along with ear reconstruction. Finally when the skeletal maturity is achieved we perform corrective bi-maxillary surgery to correct the occlusal cant and a free composite tissue transfer to achieve facial symmetry (In Detail).
Hypospedias
is a birth defect in which the urinary opening is on the under surface
(ventral surface) of the shaft of penis, or in peno-scrotal junction,
or in scrotum or way back in the perineum. The farther from the tip
of penis this opening is situated the more bent the penis is and this
deformity is called a 'chordae'.
Epispedias & Extrophy This is a birth defect resulting from failure of development of the dorsal wall of penis, anterior wall (front) of abdomen and anterior wall of the urinary bladder. While patients with Epispedias alone can develop urinary continence after surgery, for those with Extrophy achieving urinary continence is a major challenge. Syndactyly is a condition when two or more fingers are so fused that the web between them is either totally absent or incomplete. Syndactyly may be congenital (since birth) or after an improperly managed burn trauma. Either only the soft tissues are fused - simple Syndactyly or even the bones of the adjoining fingers are fused - compound Syndactyly. Surgery should be before school going age.
Duplication of a digit (finger) or a part of digit is polydactyly. Polydactyly of thumb is most commonly seen. A very meticulous surgical correction results in a perfectly functioning hand.
These are prominent outstretched ears which are a source of profound embarrassment for children going to school as they are soon picked up as 'Mickey Mouse'. A surgical correction leaves no visible scar and the child can go home the same day. (In Detail)
These are congenital malformations of the lymphatic system resulting in mono-locular or multi-locular cystic collections of straw coloured fluid. These are usually seen in the neck and face but axilla and groin are also involved. They are slow growing unless associated with internal veinous hemorrhage. They may get infected. A careful surgical excision, preserving the underlying branches of cranial nerves is the treatment. Recurrences after surgery are known.
These birth defects are cysts most commonly seen in the lateral end of eyebrows, and rarely along the mid-line in the root of nose, under the tongue, in the neck, front of chest, perineum, scrotum etc. They are just under the skin in the subcutaneous plane and can be excised surgically with minimal visible scarring.
|
|||||||||||||||||||||||||||||||||||||
